Recurrent Retroauricular Myxofibrosarcoma in Libya: A Case Report

• Misbah Elfagih

  Department of Surgery, Faculty of Medicine, Alhilal University Hospital, Misrata, Libya.

  Author

• Mohamed Elfagieh

  Department of Surgery, Faculty of Medicine, Alhilal University Hospital, Misrata, Libya.

  Author

Myxofibrosarcoma (MFS) is a rare malignant soft tissue sarcoma, typically affecting elderly patients and commonly arising from the extremities. Its occurrence in older individuals with atypical locations, such as retroauricular, is uncommon. A 50-year-old female presented with a history of recurrent left huge retroauricular mass, a painless and hard mass, not mobile, not tender, attached to the skin, approximately 4*3 cm. Initial imaging suggested a benign lesion; however, histopathological results of the excised mass revealed a spindle cell neoplasm with a lot of myxoid changes that indicate High-grade Myxofibrosarcoma. Immunohistochemistry confirmed a diagnosis of high-grade MFS. The patient underwent surgical excision of the retroauricular mass with clear margins and remains under regular follow-up with no signs of recurrence to date. In this case, the diagnostic tools of MFS are mainly used in elderly patients with atypical anatomical locations. The imaging is a nonspecific tool to confirm diagnosis, and the histopathological examination is an accurate diagnostic tool for MFS. The mainstay of MFS treatment is surgical excision, and in this case, the patient received Adjuvant Radiotherapy and systemic chemotherapy therapy (doxorubicin and ifosfamide) due to high-grade or multiple recurrences, adjuvant therapy and Regular follow- up; are essential to prevent local recurrence. This case contributes to the limited data on MFS in sub-Saharan Africa, to increase awareness and reporting, and to better understand epidemiology and management strategies in this region.

• pdf